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疾病ID:TCMBANKDI027451


疾病名:Familial pulmonary arterial hypertension


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UMLS_Name:Disease or Syndrome


DO_Name:-


疾病类型:disease


DisGeNET_Link:C1701939


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HPO_Link:-


UMLS_Link:T047


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   疾病对应的植物
ID 拉丁名 药名 药用植物名 功能与主治 来源 药用部位 使用民族

   疾病对应的化合物
化合物ID 化合物名 别名 分子式 分子质量 Smiles

   疾病对应的靶点
靶点ID 基因名 基因别名 描述
TCMBANKGE000070 CAV1 BSCL3; CGL3; LCCNS; MSTP085; PPH3; VIP21 caveolin 1
TCMBANKGE000915 BMPR2 BMPR-II; BMPR3; BMR2; BRK-3; POVD1; PPH1; T-ALK bone morphogenetic protein receptor type 2
TCMBANKGE006975 THBS1 THBS; THBS-1; TSP; TSP-1; TSP1 thrombospondin 1
TCMBANKGE003590 SMAD9 MADH6; MADH9; PPH2; SMAD8; SMAD8/9; SMAD8A; SMAD8B SMAD family member 9
TCMBANKGE011827 KCNK3 K2p3.1; OAT1; PPH4; TASK; TASK-1; TASK1; TBAK1 potassium two pore domain channel subfamily K member 3
TCMBANKGE001179 SMAD2 JV18; JV18-1; MADH2; MADR2; hMAD-2; hSMAD2 SMAD family member 2
TCMBANKGE013523 ENG END; HHT1; ORW1 endoglin
TCMBANKGE000769 EIF2AK4 GCN2; PVOD2 eukaryotic translation initiation factor 2 alpha kinase 4
TCMBANKGE003539 PAH PH; PKU; PKU1 phenylalanine hydroxylase
TCMBANKGE010841 ACVRL1 ACVRLK1; ALK-1; ALK1; HHT; HHT2; ORW2; SKR3; TSR-I activin A receptor like type 1